FIG 2. Case 2.

A, Contrast-enhanced CT scan obtained at 17 days of life shows a widening of the right lateral ventricle and sylvian fissure and areas of slight hyperdensity in the right temporooccipital region. (Courtesy of Dr. Nadia Colombo, Milan, Italy.)

B, Axial T2-weighted MR image (3000/120/1) obtained at 4 months of age shows an increase in size of the right lateral ventricle and a widening of the right hemispheric subarachnoid spaces. A lack of insular opercularization and cortical dysplasia in the right temporoparietooccipital region is well seen; the abnormal cortex is thicker than normal, with multiple and small gyri.

C and D, MR study obtained at 16 months of age. Coronal reconstruction image obtained with the MP-RAGE technique (C) confirms cortical dysplasia; the temporal cortex appears thick, with irregular gyri. On axial T2 weighted image (3000/120/1) (D), myelination seems to be normal.