FIG 1. LS SURF-1. Case 5. Male patient, 2 years old.

A–C, Axial T2-weighted images (3000/120/1 [TR/TE/NEX]) show hyperintense lesions involving the region of the inferior olivary nuclei (arrow in A) and the dorsolateral medulla at the base of the restiform bodies (arrowhead in A), punctuate lesions in the pontine tegmentum (arrowhead in B) and more extensive abnormalities in the cerebellar white matter, and lesions in the periaqueductal area and subthalamic nuclei (arrowhead in C).

D and E, Coronal T2-weighted sections (3000/120/1) confirm the presence of lesions in the subthalamic nuclei (arrowhead in D) and show extensive white matter involvement of the cerebellum centered on the dentate nuclei (in E).