Fig 2. Axial and coronal FLAIR images in patient 6 show signal intensity changes prevalent in the cerebral posterior periventricular regions (A and B) and involvement of the hilum of the dentate nuclei (arrow on the left side, B). In patient 11, coronal FLAIR image (C) shows a thin bilateral band of periventricular hyperintensity (arrowheads on the right) not recognizable on T2-weighted images (not shown). In patient 3, midbrain peripheral rim of hyperintensity (arrow) is seen only on FLAIR section (D).