American Journal of Neuroradiology 24:835-837, May 2003
© 2003 American Society of Neuroradiology
Case Report
PEDIATRICS
Tuberous Sclerosis and Fibrous Dysplasia
a the section of Diagnostic Radiology, Department of Internal Medicine, University of Parana School of Medicine, Curitiba, Parana, Brazil
b Neuropediatrics Section of the Hospital de Clinicas of the University of Parana, Curitiba, Parana, Brazil
Address correspondence to Emerson L. Gasparetto, M.D., Av. Silva Jardim 296 ap.502, CEP: 80230000, Curitiba, Paraná, Brazil
Summary: We present the case of an 11-year-old female patient with tuberous sclerosis who had a right nasal mass. CT examination revealed fibrous dysplasia involving the frontal, ethmoid, sphenoid, and vomer bones. Biopsy findings of the mass confirmed this diagnosis, and follow-up revealed marked expansion of these lesions. The authors emphasize the association of bone abnormalities and tuberous sclerosis and discuss the consideration of fibrous dysplasia as a component of this syndrome.