Advanced

AJNR - American Journal of Neuroradiology

This Article Figures Only Full Text Full Text (PDF) Alert me when this article is cited Alert me if a correction is posted Citation Map Services Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Download to citation manager Citing Articles Citing Articles via HighWire Citing Articles via CrossRef Citing Articles via Google Scholar Google Scholar Articles by Zhang, W. Articles by Papanicolaou, A. C. Search for Related Content PubMed PubMed Citation Articles by Zhang, W. Articles by Papanicolaou, A. C.

American Journal of Neuroradiology 24:1468-1470, August 2003
© 2003 American Society of Neuroradiology

Case Report
PEDIATRIC

Neuroimaging Features of Epidermal Nevus Syndrome

Wenbo Zhang^a, Panagiotis G. Simos^a, Hideaki Ishibashi^a, James W. Wheless^b,c, Eduardo M. Castillo^a, Joshua I Breier^a, James E. Baumgartner^b, Michele E. Fitzgerald^a and Andrew C. Papanicolaou^a

^a Department of Neurosurgery, Vivian L. Smith Center for Neurologic Research, Texas Comprehensive Epilepsy Program, The University of Texas Health Science Center at Houston, Houston, TX
^b Department of Pediatrics, Vivian L. Smith Center for Neurologic Research, Texas Comprehensive Epilepsy Program, The University of Texas Health Science Center at Houston, Houston, TX
^c Department of Neurology,Vivian L. Smith Center for Neurologic Research, Texas Comprehensive Epilepsy Program, The University of Texas Health Science Center at Houston, Houston, TX

Address reprint requests to Wenbo Zhang, MD, PhD, Vivian L. Smith Center for Neurologic Research, Section of Clinical Neuroscience, Department of Neurosurgery, The University of Texas Health Science Center at Houston, 1133 Moursund Street Suite H114, Houston, TX 77030

Summary: Epidermal nevus syndrome is a kind of neurocutaneous syndrome that is associated with epidermal nevus and a variety of congenital CNS disorders. Clinical presentations include seizures, paresis, mental retardation, and developmental delay. We report three cases with MR imaging and magnetoencephalography findings; one patient underwent ictal and interictal single photon emission CT. Both structural and functional imaging studies indicated that the frontal lobes had lesser involvement or were intact. One patient underwent hemispherectomy because of the medically intractable seizure. He remained seizure free with topiramate monotherapy.

This article has been cited by other articles:

				M. Canyigit and K.K. Oguz Epidermal Nevus Syndrome with Internal Carotid Artery Occlusion and Intracranial and Orbital Lipomas AJNR Am. J. Neuroradiol., August 1, 2006; 27(7): 1559 - 1561. [Abstract] [Full Text] [PDF]