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American Journal of Neuroradiology 27:1927-1929, October 2006
© 2006 American Society of Neuroradiology

Case Report
PEDIATRICS

Dural Arteriovenous Malformation in a Child with Bannayan-Riley-Ruvalcaba Syndrome

R.N. Srinivasaa,b and P.E. Burrowsa

a Department of Radiology, Children’s Hospital, Boston, Mass
b Texas Tech University School of Medicine, El Paso, Tex

Please address correspondence to: Ravi N. Srinivasa, MD, 437 E. 14 Mile Rd, Birmingham, MI 48009; e-mail: ravi.srinivasa{at}beaumont.edu

SUMMARY: Intracranial arteriovenous malformations (AVM) are a rare feature of Bannayan-Riley-Ruvalcaba syndrome (BRRS). Palencia et al reported a case of intracranial arteriovenous malformation in a child with BRRS in a Spanish journal in 1986. However, the occurrence of dural AVM in a patient with BRRS has not since been addressed in the literature. Advancements in imaging and therapeutic embolization, and the ability now to screen for phosphatase and tensin homologue (PTEN) mutations allow us to detect and manage these patients sooner. Early detection of intracranial AVMs is necessary because of the risk for progression to venous ischemia and resultant neurologic damage. We present the case of a child with headaches and periorbital venous congestion due to a dural AVM with bilateral venous outflow occlusion who was treated with multiple embolizations, now with interval remission of headache symptoms.




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Copyright © 2009 by the American Society of Neuroradiology. Print ISSN: 0195-6108 Online ISSN: 1936-959X