American Journal of Neuroradiology 28:1160-1161, June-July 2007
DOI 10.3174/ajnr.A0485
© 2007 American Society of Neuroradiology
Case Report
HEAD & NECK
Melnick-Needles Syndrome: Report of a Case Associated with Bilateral Hypoplasia of the Cochlea
a From Royal Hallamshire Hospital, Sheffield Teaching Hospitals National Health Service Trust, Sheffield, England
Please address correspondence to Jane C. Belfield, MD, Radiology Department, C Floor, Royal Hallamshire Hospital, Glossop Rd, Sheffield, S10 2JF, England; e-mail: jane.belfield{at}virgin.net
SUMMARY: Melnick-Needles Syndrome is a rare disorder associated with many abnormalities. This case report describes a patient with Melnick-Needles Syndrome who was found to have bilateral hypoplasia of the cochlea, a finding not previously described in the literature. The case report describes the syndrome and demonstrates the findings on CT and MR imaging of temporal bones.