Abnormalities in the Cerebral Arterial System in Osteogenesis Imperfecta
Sait Albayrama,
Osman Kizilkilica,
Halit Yilmaza,
Beyhan Tuysuzb,
Naci Kocera and
Civan Islaka
a Department of Radiology, Division of Neuroradiology, Cerrahpasa Medical School, Istanbul University, Turkey
b Department of Pediatrics, Division of Genetics, Cerrahpasa Medical School, Istanbul University, Turkey

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FIG 1. Axial proton densityweighted MR image shows linear, signal-void structures in the right basal ganglial areas and contour irregularities in the left MCA (arrow).
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FIG 2. Left ICA angiograms.
A, Anteroposterior projection reveals severe stenosis of the proximal cavernous segment of the left ICA and prethrombotic stenosis (arrow) in the M1 segment of the left MCA. Note the moyamoya-like collateral vascular structure around the proximal portion of the left MCA.
B, Right anteroposterior arteriogram also shows severe stenosis (arrow) of the proximal cavernous segment of the right ICA.
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