Blue Rubber-Bleb Nevus Syndrome: Report of a Familial Case with a Dural Arteriovenous Fistula
Sílvia Carvalhoa,
Vieira Barbosab,
Nuno Santosa and
Egidio Machadoa
a Department of Neuroradiology, Hospitais da Universidade de Coimbra, Portugal
b Department of Neurology, Hospitais da Universidade de Coimbra, Portugal

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FIG 1. MR images obtained on admission.
A, Axialproton density-weighted image (2530/25 [TR/TE]) shows enlarged veins in the posterior fossa.
B, Sagittal T1-weighted image (450/15) shows an enlarged straight sinus and the presence of a falcine sinus. Note the tonsillar prolapse.
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FIG 2. Carotid and vertebral angiograms.
A, Left common carotid artery angiogram demonstrates a DAVF in the torcular region. It is supplied by both the occipital and middle meningeal arteries and drains in a retrograde fashion in the superior sagittal and straight sinuses. Note the presence of a falcine sinus.
B, Venous phase of a left vertebral angiogram shows substantial venous stagnation in the posterior fossa. Note the dilated premedullary and retromedullary veins.
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