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AJNR - American Journal of Neuroradiology

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Charcot-Marie-Tooth Disease: Extensive Cranial Nerve Involvement on CT and MR Imaging

Todd R. Aho^a, Robert C. Wallace^a, Alan M. Pitt^a and Kumaraswamy Sivakumar^b

^a Section of Neuroradiology, St. Joseph’s Hospital and Medical Center, Barrow Neurologic Institute, Phoenix, AZ
^b Division of Neurology, Neuromuscular Diseases Section, St. Joseph’s Hospital and Medical Center, Barrow Neurologic Institute, Phoenix, AZ

View larger version (8K): [in a new window]   FIG 1. Limited family tree demonstrates the affected members of the patient’s family, with current patient marked with arrow. (Modified from reference 6).

View larger version (161K): [in a new window]   FIG 2. A–C, Thin-section (1-mm) coronal and axial CT images of the skull base obtained with an edge-enhancing bone algorithm show enlargement (arrows) of the mastoid canals of cranial nerve VII (A), the foramina of ovale (B), and rotundum (C) bilaterally.

View larger version (155K): [in a new window]   FIG 3. Thin-section (2.5-mm) axial T1-weighted spoiled gradient-echo gadolinium-enhanced images of the brain obtained at 1.5 T for Gamma knife localization (trigeminal neuralgia). Cranial nerve enlargement (arrows) is most pronounced involving the mastoid or descending segments of cranial nerve VII (A), cisternal segments of cranial nerve III (B), V3 (C), and V2 (D) segments. Faint enhancement is identified.