Kaposiform Hemangioendothelioma Arising from the Internal Auditory Canal
J.M. Changa,
B.J. Kwona,
M.H. Hana,b,
H.S. Kanga and
K.H. Changa,b,c
a Department of Radiology, Seoul National University College of Medicine, Seoul, Korea
b Clinical Research Institute, Seoul National University Hospital, Seoul, Korea
c Institute of Radiation Medicine, Seoul National University Medical Research Center, Seoul, Korea

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Fig 1. Initial MR image in a 6-month-old male infant. Gadolinium-enhanced T1-weighted axial image shows a small homogenous enhancing nodule in the left internal auditory canal (arrow).
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Fig 2. Follow-up MR images obtained 6 months after initial presentation.
A, Axial T2-weighted image shows a large heterogeneous expansile mass at the temporal bone.
B, Axial T1-weighted image shows intratumoral multifocal hemorrhages (arrows) and vascular flow voids that are related to hypervascularity (arrowheads).
C, Gadolinium-enhanced T1-weighted axial image shows a strongly enhancing tumor, destruction of the petrous bone, and compression of the brain stem and medial temporal lobe.
D, Temporal bone CT reveals a large soft-tissue mass with severe bone destruction in left petrous bone.
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Fig 3. Lateral projection of pre-embolization external carotid angiogram (A) reveals a hypervascular tumor (arrowheads) occupying the temporomastoid region, and postembolization common carotid angiogram (B) shows near-total devascularization of the tumor (arrowheads). PVA particles were used to occlude the intratumoral vessels.
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Fig 4. Photomicrograph of histopathologic specimen shows fascicles of spindle cells (arrowheads) admixed with small vascular channels, which is characteristic of kaposiform hemangioendothelioma (hematoxylin-eosin, original magnification x200).
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