Epidermal Nevus Syndrome with Internal Carotid Artery Occlusion and Intracranial and Orbital Lipomas
M. Canyigita and
K.K. Oguza
a Department of Radiology, Hacettepe University Faculty of Medicine, Ankara, Turkey

View larger version (60K):
[in a new window]
|
Fig 1. Sagittal T1-weighted spin-echo (TR/TE, 400/9.1 ms) (A) and coronal T2-weighted TSE (TR/TE, 3500/100 ms) images show lipomatous coloboma of the left eye (B). On the sagittal T1-weighted spin-echo (TR/TE, 400/9.1 ms) image of the medial brain, a cerebellopontine angle cistern lipoma is seen (C).
| |

View larger version (60K):
[in a new window]
|
Fig 2. A, Left cerebral hemiatrophy with cortical developmental malformation is seen on the transverse T2-weighted TSE (TR/TE, 3500/100 ms) image. Thin caliber of the left ICA is also observed.
B, T2-weighted TSE (TR/TE, 3500/100 ms) transverse image from a higher section shows the collaterals in the basal cisterns.
C, Coronal T2-weighted TSE (TR/TE; 3500/100 ms) image shows atrophy of the left cerebral hemisphere with dilated lateral ventricles and temporal cortical dysplasia. Also, subcutaneous fat is diffusely thicker over the left frontotemporoparietal cranium.
| |

View larger version (71K):
[in a new window]
|
Fig 3. Time-of-flight MR angiogram (TR/TE; 39/3.26) shows thin-caliber left ICA in all intracranial segments, with a tapering end and occlusion of the artery at its bifurcation.
| |