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AJNR - American Journal of Neuroradiology

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Melnick-Needles Syndrome: Report of a Case Associated with Bilateral Hypoplasia of the Cochlea

J.C. Belfield^a, J.S. Witana^a and D.J.A. Connolly^a

^a From Royal Hallamshire Hospital, Sheffield Teaching Hospitals National Health Service Trust, Sheffield, England

View larger version (67K): [in this window] [in a new window]   Fig 1. A, Axial CT image demonstrates bone dysplasia, typical in Melnick-Needles Syndrome. B, Axial CT image through the cochlea demonstrates fluid in the middle ear and lack of a basal turn with no modiolus, consistent with hypoplasia of the cochlea. Prominent eyes can be seen.

View larger version (91K): [in this window] [in a new window]   Fig 2. A, Coronal CT reformatted image through the cochlea demonstrates lack of modiolus and a basal turn of the cochlea. B, Axial CT image demonstrates normal vestibular aqueduct and widened angle of the facial nerve at the geniculate ganglion.

View larger version (115K): [in this window] [in a new window]   Fig 3. A, Axial T2-weighted MR image shows prominent bulging eyes, as described in Melnick-Needles syndrome. B, Sagittal TI-weighted localizer demonstrates pronounced micrognathia. C, Axial T2-weighted image demonstrates hypoplasia of the cochlea.