American Journal of Neuroradiology 2008;29:306.
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American Journal of Neuroradiology
DOI 10.3174/ajnr.A0878
PEDIATRICS
Klippel-Feil Syndrome and Sprengel Deformity Combined with an Intraspinal Course of the Left Subclavian Artery and a Bovine Aortic Arch Variant
From the Departments of Pediatric Radiology (F.F., O.M., C.J., J.F.S.) and Neuropediatrics (J.L.), University Children's Hospital Basel (UKBB), Basel, Switzerland.
Please address correspondence to J.F. Schneider, MD, Department of Pediatric Radiology, University Children's Hospital UKBB, Römergasse 8, 4058 Basel, Switzerland; e-mail: jacques.schneider{at}ukbb.ch
SUMMARY: We present a case of Klippel-Feil syndrome and Sprengel deformity with a bovine aortic arch and an aberrant course of the left subclavian artery in a 14-year-old boy. CT and MR imaging of the neck and upper thorax demonstrated a cervical osseous segmentation anomaly, a left common carotid artery originating from the innominate artery, and a left subclavian artery coursing through the intraspinal space at the C6 through T1 level. Possible embryonic mechanisms and clinical significance of this variant are reviewed.