Case of the Week
Section Editors: Matylda Machnowska1 and Anvita Pauranik2
1University of Toronto, Toronto, Ontario, Canada
2BC Children's Hospital, University of British Columbia, Vancouver, British Columbia, Canada
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October 8, 2012
Orbital Venous-Lymphatic Malformation (OVLM) (Lymphangiomas)
- OVLM have been classified on the basic of anatomic location into three groups: superficial (conjunctiva and eyelid), deep (post-septal orbit), or combined lesions. Those that are superficial are usually predominantly lymphatic, while those that are deep are predominantly venous.
- OVLM often present in childhood. Swelling when superfical, and acute proptosis (when deep, secondary to intralesional hemorrhage) are common presenting features.
- Key Diagnostic Features: A multilobulated, septated, trans-spatial cystic appearing lesion is seen. Fluid-fluid levels suggestive of intralesional hemorrhage can be seen. Enhancement is variable. No flow-voids are associated with this lesion. Evaluation of the brain for associated vascular anomalies should be performed.
- DDx: hemangioma
- Rx: surgery for decompression and cosmetic purposes