Section Editor: Sandy Cheng-Yu Chen, M.D.
Taipei Medical University Hospital, Taipei, Taiwan
Figure Caption
Neurofibromatosis type 2 (NF2), an autosomal dominant phacomatosis with gene mutation at chromosome 22, is characterized by the classic imaging findings of bilateral vestibular schwannomas, multiple meningiomas, and spinal ependymoma (acronym “MISME”: multiple inherited schwannomas, meningiomas and ependymoma). MR imaging is the modality of choice to demonstrate the enhancing schwannomas (arrows in A) and other spinal tumors, such as ependymmoma (yellow arrow in B) and meningioma (red arrow in B).