PT  - JOURNAL ARTICLE
AU  - Gustavo Soto-Ares
AU  - Louise Devisme
AU  - Sylvie Jorriot
AU  - Berengere Deries
AU  - Jean P. Pruvo
AU  - Marie M. Ruchoux
TI  - Neuropathologic and MR Imaging Correlation in a Neonatal Case of Cerebellar Cortical Dysplasia
DP  - 2002 Aug 01
TA  - American Journal of Neuroradiology
PG  - 1101--1104
VI  - 23
IP  - 7
4099  - http://www.ajnr.org/content/23/7/1101.short
4100  - http://www.ajnr.org/content/23/7/1101.full
SO  - Am. J. Neuroradiol.2002 Aug 01; 23
AB  - Little documentation of the correlation between MR imaging findings in isolated cerebellar cortical dysplasia (CCD) and its neuropathologic characteristics exists in the recent literature. We documented a postmortem neuropathologic study of a clinically and radiologically well-documented case of CCD in a neonate with severe hypotonia and status epilepticus. MR imaging revealed a global vermian hypoplasia with marked cortical dysplasia. CCD was associated with a voluminous heterotopic mass. The postmortem neuropathologic study confirmed vermian hypoplasia and CCD, which consisted of right cerebellar cortical polymicrogyria with subcortical heterotopia. CCD is a pathologic entity that could be well diagnosed with MR imaging even in the neonatal period.