TY - JOUR T1 - Neurocutaneous Melanomatosis with a Rapidly Deteriorating Course JF - American Journal of Neuroradiology JO - Am. J. Neuroradiol. SP - 287 LP - 290 VL - 24 IS - 2 AU - Winnie C.W. Chu AU - Vincent Lee AU - Yu-leung Chan AU - Matthew MK Shing AU - Ki-wai Chik AU - Chi-kong Li AU - Kwok-chiu Ma Y1 - 2003/02/01 UR - http://www.ajnr.org/content/24/2/287.abstract N2 - Summary: Neurocutaneous melanosis is a rare congenital syndrome characterized by large or multiple congenital melanocytic nevi and benign or malignant pigment cell tumors of the leptomeninges. The prognosis is extremely poor for symptomatic patients, even in the absence of malignant melanoma. We present serial MR imaging findings in the brain and spine of a child with congenital giant hairy nevi who developed progressive leptomeningeal melanomatosis and whose neurologic condition rapidly deteriorated. ER -