%0 Journal Article %A Sílvia Carvalho %A Vieira Barbosa %A Nuno Santos %A Egidio Machado %T Blue Rubber-Bleb Nevus Syndrome: Report of a Familial Case with a Dural Arteriovenous Fistula %D 2003 %J American Journal of Neuroradiology %P 1916-1918 %V 24 %N 9 %X Summary: We report a case of a 45-year-old woman known to have a familial form of blue rubber-bleb nevus syndrome (BRBNS). The patient developed severe occipital headaches and bilateral retroauricular bruits. Cerebral angiography showed a large dural arteriovenous fistula in the torcular region. Central nervous system involvement in BRBNS is not often reported, and most cases of BRBNS are sporadic. %U https://www.ajnr.org/content/ajnr/24/9/1916.full.pdf