PT  - JOURNAL ARTICLE
AU  - Sun-Won Park
AU  - Hyung-Jin Kim
AU  - Hee-Seung Chin
AU  - Kee-Sun Tae
AU  - Jee-Young Han
TI  - Mesectodermal Leiomyosarcoma of the Ciliary Body
DP  - 2003 Oct 01
TA  - American Journal of Neuroradiology
PG  - 1765--1768
VI  - 24
IP  - 9
4099  - http://www.ajnr.org/content/24/9/1765.short
4100  - http://www.ajnr.org/content/24/9/1765.full
SO  - Am. J. Neuroradiol.2003 Oct 01; 24
AB  - Summary: We report a case of low-grade mesectodermal leiomyosarcoma of the ciliary body, an extremely rare tumor of neural crest origin, occurring in a 12-year-old boy. MR imaging showed a well-marginated, ovoid soft tissue mass at the right temporal ciliary body, accompanied by total retinal detachment. The mass was slightly hyperintense relative to contralateral vitreous on T1-weighted images and markedly hypointense on T2-weighted images and enhanced very well. Initial biopsy of the mass suggested a peripheral nerve sheath tumor. The mass grew rapidly after biopsy, and enucleation was performed. The final diagnosis based on histology and immunohistochemistry was a low-grade mesectodermal leiomyosarcoma. To our knowledge, this is the first reported case of a malignant form of mesectodermal leiomyoma of the ciliary body.