PT  - JOURNAL ARTICLE
AU  - Carmelo Amato
AU  - Raffaele Ferri
AU  - Maurizio Elia
AU  - Filomena Cosentino
AU  - Carmelo Schepis
AU  - Maddalena Siragusa
AU  - Massimo Moschini
TI  - Nervous System Involvement in Degos Disease
DP  - 2005 Mar 01
TA  - American Journal of Neuroradiology
PG  - 646--649
VI  - 26
IP  - 3
4099  - http://www.ajnr.org/content/26/3/646.short
4100  - http://www.ajnr.org/content/26/3/646.full
SO  - Am. J. Neuroradiol.2005 Mar 01; 26
AB  - Summary: Degos disease, or malignant atrophic papulosis, is a rare obstructive vasculopathy of unknown origin, characterized by distinctive skin lesions, visceral involvement, and an unfavorable outcome. The gastrointestinal tract and the central nervous system are most frequently affected, but cases limited to benign skin lesions have also been described. Neuroradiologic reports of this condition are exceptionally rare. We report the case of a 29-year-old woman with central and peripheral nervous system involvement who presented with progressive clinical deterioration and a meningovascular pattern at cerebral MR imaging; other organs were spared in this patient.