TY - JOUR T1 - Cranial CT findings in sclerosteosis. JF - American Journal of Neuroradiology JO - Am. J. Neuroradiol. SP - 505 LP - 511 VL - 7 IS - 3 AU - S C Hill AU - S A Stein AU - A Dwyer AU - J Altman AU - R Dorwart AU - J Doppman Y1 - 1986/05/01 UR - http://www.ajnr.org/content/7/3/505.abstract N2 - Sclerosteosis or Van Buchem's disease is a rare genetic craniotubular hyperostosis that becomes evident in early childhood and is associated with progressive involvement of the skull. The pathologic changes in the cranium noted on CT are described in three cases. Although the disease is incurable, CT is useful to display the morbid anatomy of the cranium before palliative surgery. ER -