PT  - JOURNAL ARTICLE
AU  - B.Y. Huang
AU  - C. Zdanski
AU  - M. Castillo
TI  - Pediatric Sensorineural Hearing Loss, Part 2: Syndromic and Acquired Causes
AID  - 10.3174/ajnr.A2499
DP  - 2011 May 18
TA  - American Journal of Neuroradiology
4099  - http://www.ajnr.org/content/early/2011/05/19/ajnr.A2499.short
4100  - http://www.ajnr.org/content/early/2011/05/19/ajnr.A2499.full
AB  - SUMMARY: This article is the second in a 2-part series reviewing neuroimaging in childhood SNHL. Previously, we discussed the clinical work-up of children with hearing impairment, the classification of inner ear malformations, and congenital nonsyndromic causes of hearing loss. Here, we review and illustrate the most common syndromic hereditary and acquired causes of childhood SNHL, with an emphasis on entities that demonstrate inner ear abnormalities on cross-sectional imaging. Syndromes discussed include BOR syndrome, CHARGE syndrome, Pendred syndrome, Waardenburg syndrome, and X-linked hearing loss with stapes gusher. We conclude the article with a review of acquired causes of childhood SNHL, including infections, trauma, and neoplasms.