RT Journal Article
SR Electronic
T1 Cranial CT and MR in the Klippel-Trenaunay-Weber syndrome.
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 291
OP 294
VO 13
IS 1
A1 Williams, D W
A1 Elster, A D
YR 1992
UL http://www.ajnr.org/content/13/1/291.abstract
AB This report describes the intracranial CT and MR findings in two cases of Klippel-Trenaunay-Weber Syndrome. The findings are 1) markedly enhancing choroid plexuses, 2) severe cerebral atrophy, 3) cerebral calcifications, and 4) angiomatous leptomeningeal enhancement. The findings may resemble those seen in cases of bilateral Sturge-Weber syndrome. The two diseases should be distinguishable by the external stigmata. The authors raise the question of a spectrum of involvement in the angiodysplasias of Klippel-Trenaunay-Weber syndrome and Sturge-Weber syndrome with considerable overlap.