RT Journal Article
SR Electronic
T1 Oromaxillofacial Osseous Abnormality in Sturge-Weber Syndrome: Case Report and Review of the Literature
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 274
OP 277
VO 27
IS 2
A1 D.D.M. Lin
A1 P. Gailloud
A1 E.F. McCarthy
A1 A.M. Comi
YR 2006
UL http://www.ajnr.org/content/27/2/274.abstract
AB SUMMARY: We report a case of a 17-month-old child affected by Sturge-Weber syndrome who had unusually rapid overgrowth of the left frontal, temporal, orbital, and maxillary regions. CT angiography illustrated osteohypertrophy with periostitis and associated soft tissue hypertrophy directly corresponding to the distribution of the cutaneous port-wine stain. Extended maxillectomy was performed because of rapid growth and clinical debilitation, with surgical pathology revealing juvenile ossifying fibroma.