TY - JOUR T1 - Pantothenate Kinase-Associated Neurodegeneration with Increased Lentiform Nuclei Cerebral Blood Flow JF - American Journal of Neuroradiology JO - Am. J. Neuroradiol. SP - 212 LP - 213 VL - 27 IS - 1 AU - M. Koyama AU - A. Yagishita Y1 - 2006/01/01 UR - http://www.ajnr.org/content/27/1/212.abstract N2 - Summary: We report a case of pantothenate kinase-associated neurodegeneration with increased regional cerebral blood flow (rCBF) in bilateral lentiform nuclei on technetium Tc-99m ethyl cysteinate dimer single-photon emission CT (ECD-SPECT). A 6-year-old boy presented with opisthotonus. T2*-weighted MR images revealed areas of marked hypointensity with a hyperintense focus in bilateral globus pallidus, creating the characteristic eye-of-the-tiger appearance. ECD-SPECT showed increased rCBF in bilateral lentiform nuclei. ER -