PT  - JOURNAL ARTICLE
AU  - J.K. Weeks
AU  - K.J. Helton
AU  - M.E. Conley
AU  - M. Onciu
AU  - R.B. Khan
TI  - Diffuse CNS Vasculopathy with Chronic Epstein-Barr Virus Infection in X-Linked Lymphoproliferative Disease
DP  - 2006 Apr 01
TA  - American Journal of Neuroradiology
PG  - 884--886
VI  - 27
IP  - 4
4099  - http://www.ajnr.org/content/27/4/884.short
4100  - http://www.ajnr.org/content/27/4/884.full
SO  - Am. J. Neuroradiol.2006 Apr 01; 27
AB  - SUMMARY: We report a patient with X-linked lymphoproliferative disease (XLP) who developed multiple central nervous system (CNS) manifestations of Epstein-Barr virus infection. XLP, or Duncan syndrome, is a rare inherited disorder characterized by the inability to clear Epstein-Barr virus infection. In addition to Epstein-Barr virus encephalitis, CNS lymphoproliferative disease, and lymphoma, this patient also developed MR angiographic evidence of diffuse fusiform aneurysmal dilation of intracranial vessels.