TY - JOUR T1 - Serial MR Imaging, Diffusion Tensor Imaging, and MR Spectroscopic Findings in a Child with Progressive Encephalopathy, Edema, Hypsarrhythmia, and Optic Atrophy (PEHO) Syndrome JF - American Journal of Neuroradiology JO - Am. J. Neuroradiol. SP - 1555 LP - 1558 VL - 27 IS - 7 AU - T.A.G.M. Huisman AU - A. Klein AU - B. Werner AU - T. Straube AU - E. Boltshauser Y1 - 2006/08/01 UR - http://www.ajnr.org/content/27/7/1555.abstract N2 - SUMMARY: PEHO syndrome is a rare symptom complex of severe progressive encephalopathy, edema, hypsarrhythmia, and optic atrophy. Disease onset is in early infancy. The current case report presents and discusses serial conventional MR imaging findings and serial functional studies including diffusion tensor imaging and quantitative MR spectroscopy findings in a 6-year-old child with PEHO. ER -