PT  - JOURNAL ARTICLE
AU  - T.A. Stark
AU  - A.M. McKinney
AU  - C.S. Palmer
AU  - R.H. Maisel
AU  - C.L. Truwit
TI  - Dilation of the Subarachnoid Spaces Surrounding the Cranial Nerves with Petrous Apex Cephaloceles in Usher Syndrome
AID  - 10.3174/ajnr.A1283
DP  - 2009 Feb 01
TA  - American Journal of Neuroradiology
PG  - 434--436
VI  - 30
IP  - 2
4099  - http://www.ajnr.org/content/30/2/434.short
4100  - http://www.ajnr.org/content/30/2/434.full
SO  - Am. J. Neuroradiol.2009 Feb 01; 30
AB  - SUMMARY: Limited studies of brain MR imaging findings in Usher syndrome have reported atrophy with enlarged subarachnoid spaces. However, the specific appearance of the subarachnoid spaces surrounding the cranial nerves has not yet been described. Herein we describe the skull base MR imaging findings in an adult with Usher syndrome. Multiple cranial nerve exits were enlarged to the point of causing cephaloceles with bony remodeling. A combination of uncommon findings in this rare disorder raises the question of an etiologic association.