TY - JOUR T1 - Neuroimaging Appearance of Cerebral Malignant Epithelioid Glioneuronal Tumors in Children JF - American Journal of Neuroradiology JO - Am. J. Neuroradiol. SP - 1740 LP - 1744 DO - 10.3174/ajnr.A6668 VL - 41 IS - 9 AU - G. Orman AU - S. Mohammed AU - H.D.B. Tran AU - F.Y. Lin AU - A. Meoded AU - N. Desai AU - T.A.G.M. Huisman AU - S.F. Kralik Y1 - 2020/09/01 UR - http://www.ajnr.org/content/41/9/1740.abstract N2 - SUMMARY: Malignant epithelioid glioneuronal tumor is a rare high-grade, aggressive brain tumor that shows both glial and neuronal differentiation on histopathology but is not included in the current World Health Organization classification. The neuroimaging appearance is variable but may be secondary to the size of the mass and/or location of the tumor. In our series, all epithelioid glioneuronal tumors were encountered in the supratentorial space and included pineal, temporal, and extratemporal lobar cerebral hemisphere locations. When large, the tumors demonstrate cystic degeneration and necrosis, hemorrhage, contrast enhancement, and regions of low apparent diffusion coefficient scalars consistent with patterns seen with other high-grade pediatric brain tumors. The tumors also have a propensity to spread into the meninges at presentation and for distant CSF spread on follow-up imaging.MEGNTmalignant epithelioid glioneuronal tumor ER -