PT - JOURNAL ARTICLE AU - G Fariello AU - C Dionisi-Vici AU - C Orazi AU - S Malena AU - A Bartuli AU - P Schingo AU - E Carnevale AU - I Saponara AU - G Sabetta TI - Cranial ultrasonography in maple syrup urine disease. DP - 1996 Feb 01 TA - American Journal of Neuroradiology PG - 311--315 VI - 17 IP - 2 4099 - http://www.ajnr.org/content/17/2/311.short 4100 - http://www.ajnr.org/content/17/2/311.full SO - Am. J. Neuroradiol.1996 Feb 01; 17 AB - We performed serial cranial ultrasonography in four newborns affected by maple syrup urine disease. Symmetric increase of echogenicity of periventricular white matter, basal ganglia (mainly pallidi), and thalami was detected in the acute stage. The degree of ultrasonography abnormalities paralleled the clinical course of the disease.