Table 1:

Orbital LM Characteristics

LocationNo.MacroMicroCombinedIntraconal*Extraconal*Periorbital*Diffuse
Frontal71511343
Frontotemporal41211122
Cranial base10100010
Lower cervicofacial51400023
Cheek & frontal31201121
Cervicofacial & frontotemporal11001100
Cheek41211013
Bilateral cervicofacial20111101
Isolated orbital62313222
Total338205981415
  • Note:—LM indicates lymphatic malformation; diffuse, intraconal + extraconal + periorbital; macro, macrocystic; micro, microcystic; combined, macrocystic and microcystic components.

  • * Alone or associated with intraconal or extraconal or periorbital lesions.