Summary of reported cases of Klippel-Trenaunay-Weber Syndrome associated with spinal arteriovenous malformations
| Study | Year | Reported AVM(s) | Age and Sex of Patient | AVM Location | Type | Comments |
|---|---|---|---|---|---|---|
| Den Hartog Jager16 | 1949 | 1 | 27 years, male | Spine (T9–T10) | Intramedullary* | |
| Schulz et al30 | 1966 | 1 | 24 years, male | Spine (T5–T7) | Not specified | |
| Krayenbühl et al23 | 1970 | 1 | 20 years, male | Spine (T5–T9) | Extradural | Presented as leg spasticity |
| Förster and Kazner18 | 1973 | 1 | 11 years, female | Spine (T9–L2) | Intramedullary | |
| Saito et at26 | 1975 | 1 | 49 years, female | Spine (T4–L4) | Spinal cord | |
| Pitagoras de Mattos25 | 1975 | 1 | 33 years, male | Spine (T9–T10) | Intramedullary* | |
| Eber et al17 | 1976 | 1 | 32 years, male | Spine (L1) | Intramedullary* | |
| Djindjian et al5 | 1977 | 5 | 13 years, male | Spine (T9–T12) | Intramedullary* | |
| 22 years, female | Spine (T5–T6) | Intramedullary* | ||||
| 28 years, male | Spine (T9–L2) | Intramedullary* | ||||
| 13 years, female | Spine (L1–L2) | Intramedullary* | ||||
| 15 years, male | Spine (L1–L2) | Intramedullary* | ||||
| Vajda et al29 | 1983 | 1 | 10 years, male | Spine (T12–L2) | Intramedullary* | |
| Benhaiem-Sigaux et al15 | 1985 | 1 | 9 years, female | Spine (T11–T12) | Extramedullary | Presented with headache, lower limb pain, weakness, and swallowing difficulties |
| Komatsu et al22 | 1985 | 1 | 13 years, male | Spine (L4–L5) | Not specified | |
| Jyoichi et al20 | 1989 | 1 | 67 years, male | Spine | Not specified | |
| Kojima et al21 | 1989 | 1 | 28 years, female | Spine (T11–L2) | Spinal cord | 4-month history of steadily progressive weakness and dysesthesia |
| Tan et al28 | 1990 | 2 | 19 years, male | Spine (T2–T6 and T10–T12) | Juvenile/glomus | Sudden onset of thoracic pain and paraplegia, severe impairment of all sensory modalities below T4 level and bilateral clonus |
| Nakstad et al24 | 1993 | 4 | 13 years, female | Spine (T11–T12) | Extramedullary | |
| Szajner et al27 | 1999 | 1 | 48 years, female | Spine (C6–C7) | Epidural | |
| Alexander et al3 | 2002 | 1 | 30 years, male | Spine (T3–T4) | Extradural | 10-month history of progressive myelopathy, bilateral lower-extremity weakness, and numbness |
* Subtype not specified.