TABLE 1:

Neuroradiologic findings

Patient No./Age (y)/SexLocationSize (cm)SymptomsBony AnomaliesNECT (Compared to Brain)T1WI (Compared to CSF)T2WI (Compared to Brain)FLAIR (Compared to CSF)T1 C+ (Enhancement)DWI (Restriction)
1/46/FRight lower CPA1.2 × 0.8 × 0.6Decreased gag reflex on right, decreased sensation in right VI and V3 nervesIsodenseHyperintenseHyperintenseHyperintenseNoneNone
2/26/FMidline, right lower CPA2.6 × 1.6Right-sided paresthesias, chronic migraine headachesHyperintenseHypointenseHyperintenseNone
3/39/F*Midline, pontomedullary junction0.6 × 1.4 × 1.1Chronic headachesHyperintenseHyperintenseHyperintenseNoneMild
4/72/FLeft frontal lobe8.8 × 4.6 × 6.6Behavior changes leading to psychosisHypodenseHyperintenseHyperintenseHyperintenseNone
5/60/FMidline, pontomedullary junction1.5 × 0.8Chronic headachesHyperintenseHyperintense
6/unknown*Lateral pontomedullary junction1.5 × 1HyperintenseHyperintenseHyperintensePosterior rim (at brain)
7/41/FMidline, lower CPA2.5 × 1.5Chronic headache, tingling in distal extremitiesHyperintenseHyperintensePosterior rim (at brain)
8/57/FMidline, 4th ventricle3.4 × 3 × 2.5Occasional vertigo, chronic occipital headacheHyperintenseHyperintenseNone
9/12/FMidline, lower CPA1.4 × 1.8 × 0.8History of recurrent meningitisMidline cleft, CVJHyperintenseHyperintenseHyperintense
10/70/MMidline to right lower CPA3 × 4Incontinence, inability to walkHyperintenseHyperintense
11/26/FMidline, anterior to medulla1.5 × 22 episodes “viral syndrome” (headache, fever nausea, vomiting, nuchal rigidity, fever)HyperintenseHyperintensePosterior rim (at brain)
12/34/MLeft of midline, adjacent to calvarium, extending through left ethnoid9 × 6 × 7New onset seizuresHypodenseIsointenseHyperintenseNone
13/21/FMidline, anterior to brain stem extending into both CPA cisterns3 × 2.5“Migraines,” persistent occipital headachesHyperdenseHyperintenseHypointenseHyperintense
14/44/FLower left CPA3 × 3Progressive clumsiness of hands with gait disturbanceHyperintenseHyperintenseNone
15/14/FRight CPA2 × 2 × 2Long history of right-sided sensorineural hearing lossHyperintenseHyperintensePosterior rim (at brain)
16/78/FExtra-axial right frontal lobe, with fluid-fluid levels7 × 5 × 3Acute onset single seizureIsodenseIso-hyperintenseHyperintenseNone
17/48/MLeft intra/paraventricular, bilobed8 × 52 weeks of tremor, numbness of right arm, and facial droopHyperdense, marginal Ca++HyperintenseHyperintenseThin marginal enhancement
18/78/MExtra-axial, frontal lobe, multiple fluid-fluid levels7 × 5 × 3New onset seizureHypodenseHyperintenseHyperintenseNone
  • Note:—CPA indicates cerebellopontine angle; NECT, nonenhanced CT; T1WI, T1-weighted image; T2W1, T2-weighted image; T1 C+, T1 with gadolinium; DWI, diffusion-weighted image; CVJ, craniovertebral junction.

  • * Presumed neurenteric cyst