Table 1:

Clinical findings of pathologically confirmed corticobasal degeneration

Case No.Age at Onset (yr)SexDuration (yr)RigidityDystoniaPyramidal SignsCortical DysfunctionVertical Gaze PalsyDementiaCDx
174F10Lt>RtOcular apraxia+MutePSP?
268F6Lt>RtApraxia (Lt hand)±+ Severe akinetic muteAD
367M3Rt>LtNo cortical sign++ SeverePDD
474F6Rt>Lt++ SevereCBD
  • Note:—CBD indicates corticobasal degeneration; PSP?, progressive supranuclear palsy suspected; CDx, clinical diagnosis; AD, Alzheimer disease; PDD, Parkinson disease with dementia; –, no symptom; +, obvious symptom; ±, suspicious symptom; Lt, left; Rt, right.