Inner ear/IAC abnormalities in children with ANSDa
| Type of Temporal Bone Abnormality | Cochlear Nerve Status | ||
|---|---|---|---|
| Normal (n = 69) | Unilateral CND (n = 19) | Bilateral CND (n = 15) | |
| None | 68 (98.6%)1,2 | 2 (10.5%)1 | 1 (6.7%)2 |
| Any labyrinthine abnormality | 1 (1.4%)3 | 3 (15.8%)4 | 11 (73.3%)3,4 |
| Cochlear malformations | 1 (1.4%)5 | 2 (10.5%)6 | 8 (53.3%)5,6 |
| Vestibular malformations | 0 (0.0%)7 | 2 (10.5%) | 5 (33.3%)7 |
| SCC malformations | 0 (0.0%)8 | 2 (10.5%) | 4 (26.7%)8 |
| Large endolymphatic duct/sac | 1 (1.4%) | 0 (0.0%) | 0 (0.0%) |
| IAC stenosis/atresia | 0 (0.0%)9,10 | 5 (26.3%)9 | 7 (46.7%)10 |
| BCNC stenosis/atresia | 0 (0.0%)11,12 | 15 (78.9%)11 | 13 (86.7%)12 |
a Superscripts denote significant group pair differences: 1–5, 7–12, P ≤ .001; 6, P =.010.