TABLE 1:

Clinical data of sporadic CJD patients

Patient
123456
Age at onset56.2 years58.9 years71.9 years62.9 years63.6 years61 years
GenderMaleMaleMaleFemaleMaleFemale
Symptoms/signsDementia, ataxia, myoclonusDementia, vertigo, ataxiaDementia, ataxia, myoclonusDementia, vertigo, gait disturbancesDementia, ataxia, signs of pyramidal tractDementia, vertigo, ataxia
EEGNot typical for CJDNot typical for CJDPSWCsaPSWCsaPSWCsNot typical for CJD
Protein 14-3-3PositivePositivePositivePositivePositivePositive
Diagnosis of CJDbProbableProbableProbableProbableDefiniteProbable
  • a PSWCs are periodic sharp wave complexes (4).

  • b WHO 1998 (1).