Patients with NF1

LocationNo. of Patients (n=31)
Soft-tissue tumor without orbital involvement7 (22.6)
Radiologic orbital changes24 (77.4)
Distortion due to an enlarged middle cranial fossa13 (41.9)
Orbital-rim enlargement18 (58.1)
 Associated with buphthalmos13
 Associated with a small maxillary sinus13
 Associated with tumor in the anterior orbit2
Imaging evidence of tumor within the orbit19 (61.3)
 Intraconal tumor13
 Globe (buphthalmos with or without enucleation)13
 Lacrimal gland11
 Extraocular muscle13
 Posterior orbit16
 Orbital bone18
Expansion of the orbital foramen16 (51.6)
 Expansion of the superior orbital fissure15
 Expansion of the inferior orbital fissure12
 Expansion of the optic canal8
  Optic nerve glioma only6
  PNF infiltration of the optic nerve sheath2
  • Note.—Data in parentheses are percentages.