Table 1:

Clinical details of the patients with LH and LO

PatientAge (yr)SexHb GenotypeInitial Inner Ear SymptomsOther Initial SymptomsLH/LO
118MHbSCDizziness (SNHL 1 wk after initial onset)Headache, ear painLH
217MHbSCVertigoHeadache, ear painLH
313MHbSCVertigoHeadache, ear painLH
426MHbS/β-thalTinnitus, SNHLNoneLO
512MHbSSSNHLNoneLO
614FHbSSSNHLNoneLO