Age of diagnosis, y | |
Median | 9.7 |
Range | 1.8–18 |
Sex | |
Male | 7 (50%) |
Female | 7 (50%) |
MRI findings | |
NF-1 spots | 14 (100%) |
Optic nerve/chiasm thickening | 7 (50%) |
Plexiform neurofibroma | 6 (43%) |
Clinical findings | |
Headaches | 6 (43%) |
Cognitive or speech delay | 5 (36%) |
ADHD | 2 (14%) |
Note:—ADHD indicates attention deficit/hyperactivity disorder.