Table 2:

Comparison of brain MR imaging findings in patients with IVS4-type Fabry disease, with and without brain infarctions

InfarctionNoninfarctionP Valuea
No.917
Mean age (SD) (years)64.0 (5.2)56.8 (7.0).009
Sex (M/F)6:314:3.332
Area of infarction (anterior circulation/posterior circulation/both)3/2/40/0/0.012
Hemorrhage/microbleeds0 (0%)0 (0%)1.000
White matter scoresb2/4/2/113/4/0/0.023
Pulvinar sign3 (33%)5 (29%).837
Chiari I malformation0 (0%)0 (0%)1.000
Vascular stenosisc2 (22%)0 (0%).041
Mean diameter of BA (SD) (mm)2.57 (0.64)2.86 (0.61).301
Laterality of BAb4/5/0/08/8/1/0.732
Height of BA bifurcationb3/5/13/5/9.114

  • ↵a P, unadjusted.

  • ↵b Scale of 0/1/2/3.

  • ↵c Presence of focal stenosis of all intracranial arteries.