Patients with DMD (Range) | Controls (Range) | |
---|---|---|
Age at recruitment (mean) (yr) | 8.0 ± 1.2 (6–10) | 8.2 ± 1.4 (6–10) |
Age at onset (mean) (yr) | 4.1 ± 1.8 (1–9) | |
Age at presentation (mean) (range) (yr) | 7.5 ± 1.4 (4–10) | |
Duration (mean) (mo) | 40.8 ± 25.2 (6–120) | |
MDFRS domains (mean) | ||
Mobility (maximum 36) | 24.35 ± 3.272 (15–30) | |
Basic ADL (maximum 24) | 18.77 ± 2.547 (12–25) | |
Arm function (maximum 28) | 22.07 ± 1.885 (19–25) | |
Impairment (maximum 44) | 34.18 ± 3.568 (23–40) | |
Total score (maximum 132) | 99.37 ± 10.55 (69–117) |
Note:—ADL indicates activities of daily living; MDFRS, Muscular Dystrophy Functional Rating scale.