Abstract
A child with Morquio syndrome developed severe cervical kyphosis causing myelopathy. Decompression of the spinal cord was accomplished by an anterior approach using multilevel corpectomies and stabilization with calvarial bone grafts and halo immobilization. The case reported is unique in that from an uncommon degree of cervical kyphosis rather than the usual atlantoaxial instability seen in patients with Morquio syndrome. The operative procedure described shows another example of the usefulness of calvarial bone grafts for cervical spine fusions in children.
Similar content being viewed by others
References
Ashraf J, Crockard AH, Ransford AO, Stevens JM (1991) Transoral decompression and posterior stabilization in Morquio's disease. Arch Dis Child 66:1318–1321
Blaw ME, Langer LO (1969) Spinal cord compression in Morquio-Brailsford's disease. J Pediatr 74:593–600
Chadduck WM, Boop FA (1994) Use of full-thickness calvarial bone grafts for cervical spinal fusions in pediatric patients. Pediatr Neurosurg 20:107–112
Edwards MK, Harwood-Nash DC, Fitz CR, Chuang SH (1982) CT metrizamide myelography of the cervical spine in Morquio syndrome. AJNR 3:666–669
Holmes JC, Hall JE (1978) Fusion for instability and potential instability of the cervical spine in children and adolescents. Orthop Clin North Am 9:923–943
Lipson SJ (1977) Dysplasia of the odontoid process in Morquio's syndrome causing quadriparesis. J Bone Joint Surg Am 59:340–344
Nelson J, Thomas PS (1988) Clinical findings in 12 patients with MPS IVA (Morquio's disease). Further evidence for heterogeneity. III. Odontoid dysplasia. Clin Genet 33:126–130
Stabler CL, Eismont FJ, Brown MD, Green BA, Malinin TI (1985) Failure of posterior cervical fusions using cadaveric bone graft in children. J Bone Joint Surg Am 67:370–375
Stevens JM, Kendall BE, Crockard AH, Ransford A (1991) The odontiod process in Morquio-Brailsford's disease. The effects of occipito-cervical fusion. J Bone Joint Surg Br 73:851–858
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Picicirilli, C.B., Chadduck, W.M. Cervical kyphotic myelopathy in a child with Morquio syndrome. Child's Nerv Syst 12, 114–116 (1996). https://doi.org/10.1007/BF00819510
Received:
Revised:
Issue Date:
DOI: https://doi.org/10.1007/BF00819510