Skip to main content
Log in

Cervical kyphotic myelopathy in a child with Morquio syndrome

  • Case Report
  • Published:
Child's Nervous System Aims and scope Submit manuscript

Abstract

A child with Morquio syndrome developed severe cervical kyphosis causing myelopathy. Decompression of the spinal cord was accomplished by an anterior approach using multilevel corpectomies and stabilization with calvarial bone grafts and halo immobilization. The case reported is unique in that from an uncommon degree of cervical kyphosis rather than the usual atlantoaxial instability seen in patients with Morquio syndrome. The operative procedure described shows another example of the usefulness of calvarial bone grafts for cervical spine fusions in children.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

Similar content being viewed by others

References

  1. Ashraf J, Crockard AH, Ransford AO, Stevens JM (1991) Transoral decompression and posterior stabilization in Morquio's disease. Arch Dis Child 66:1318–1321

    PubMed  Google Scholar 

  2. Blaw ME, Langer LO (1969) Spinal cord compression in Morquio-Brailsford's disease. J Pediatr 74:593–600

    PubMed  Google Scholar 

  3. Chadduck WM, Boop FA (1994) Use of full-thickness calvarial bone grafts for cervical spinal fusions in pediatric patients. Pediatr Neurosurg 20:107–112

    PubMed  Google Scholar 

  4. Edwards MK, Harwood-Nash DC, Fitz CR, Chuang SH (1982) CT metrizamide myelography of the cervical spine in Morquio syndrome. AJNR 3:666–669

    PubMed  Google Scholar 

  5. Holmes JC, Hall JE (1978) Fusion for instability and potential instability of the cervical spine in children and adolescents. Orthop Clin North Am 9:923–943

    PubMed  Google Scholar 

  6. Lipson SJ (1977) Dysplasia of the odontoid process in Morquio's syndrome causing quadriparesis. J Bone Joint Surg Am 59:340–344

    PubMed  Google Scholar 

  7. Nelson J, Thomas PS (1988) Clinical findings in 12 patients with MPS IVA (Morquio's disease). Further evidence for heterogeneity. III. Odontoid dysplasia. Clin Genet 33:126–130

    PubMed  Google Scholar 

  8. Stabler CL, Eismont FJ, Brown MD, Green BA, Malinin TI (1985) Failure of posterior cervical fusions using cadaveric bone graft in children. J Bone Joint Surg Am 67:370–375

    Google Scholar 

  9. Stevens JM, Kendall BE, Crockard AH, Ransford A (1991) The odontiod process in Morquio-Brailsford's disease. The effects of occipito-cervical fusion. J Bone Joint Surg Br 73:851–858

    PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Rights and permissions

Reprints and permissions

About this article

Cite this article

Picicirilli, C.B., Chadduck, W.M. Cervical kyphotic myelopathy in a child with Morquio syndrome. Child's Nerv Syst 12, 114–116 (1996). https://doi.org/10.1007/BF00819510

Download citation

  • Received:

  • Revised:

  • Issue Date:

  • DOI: https://doi.org/10.1007/BF00819510

Key words

Navigation