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Anatomic and Quantitative Temporal Bone CT for Preoperative Assessment of Branchio-Oto-Renal Syndrome

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Abstract

We describe the temporal bone computed tomography (CT) findings of an unusual case of branchio-oto-renal syndrome with ectopic ossicles that are partially located in the middle cranial fossa. We also describe quantitative temporal bone CT assessment pertaining to cochlear implantation in the setting of anomalous cochlear anatomy associated with this syndrome.

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References

  1. Soriano JR. Branchio-oto-renal syndrome. J Nephrol. 2003;16:603–5.

    CAS  Google Scholar 

  2. Fraser FC, Ling D, Clogg D, Nogrady B. Genetic aspects of the BOR syndromebranchial fistulae, ear pits, hearing loss, and renal anomalies. Am J Med Genet. 1978;72:241–52.

    Article  Google Scholar 

  3. Propst EJ, Blaser S, Gordon KA, Harrison RV, Papsin BC. Temporal bone findings on computed tomography imaging in branchio-oto-renal syndrome. Laryngoscope. 2005;115:1855–62.

    Article  PubMed  Google Scholar 

  4. Ceruti S, Stinckens C, Cremers CW, Casselman JW. Temporal bone anomalies in the branchio-oto-renal syndrome: detailed computed tomographic and magnetic resonance imaging findings. Otol Neurotol. 2002;23:200–7.

    CAS  Google Scholar 

  5. Supakul N, Kralik SF, Ho CY. Ectopic external auditory canal and ossicular formation in the oculo-auriculo-vertebral spectrum. Pediatr Radiol. 2015;45:1099–102.

    Article  PubMed  Google Scholar 

  6. Kameswaran M, Kumar RS, Murali S, Raghunandhan S, Karthikeyan K., Cochlear implantation in branchio-oto-renal syndrome—A surgical challenge. Indian J Otolaryngol Head Neck Surg. 2007;59:280–3.

    Article  PubMed  PubMed Central  Google Scholar 

  7. Buchman CA, Copeland BJ, Yu KK, Brown CJ, Carrasco VN, Pillsbury HC 3rd. Cochlear implantation in children with congenital inner ear malformations. Laryngoscope. 2004;114:309–16.

    Article  PubMed  Google Scholar 

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Authors and Affiliations

  1. Department of Radiology, Pritzker School of Medicine, University of Chicago, 5841 S Maryland Avenue, 60637, Chicago, IL, USA

    D. T. Ginat MD, MS

  2. Audiology Department, University of Chicago Medical Center, Chicago, IL, USA

    L. Ferro AuD

  3. Section of Otolaryngology-Head & Neck Surgery, Pritzker School of Medicine, University of Chicago, Chicago, IL, USA

    M. B. Gluth MD

Authors
  1. D. T. Ginat MD, MS
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  2. L. Ferro AuD
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  3. M. B. Gluth MD
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Corresponding author

Correspondence to D. T. Ginat MD, MS.

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None of the authors have conflicts of interest.

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Ginat, D.T., Ferro, L. & Gluth, M.B. Anatomic and Quantitative Temporal Bone CT for Preoperative Assessment of Branchio-Oto-Renal Syndrome. Clin Neuroradiol 26, 481–483 (2016). https://doi.org/10.1007/s00062-016-0502-7

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  • DOI: https://doi.org/10.1007/s00062-016-0502-7

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