Abstract
We present a case of Sturge-Weber syndrome with a bilateral lymphatic/venous malformation of the mandible. Modern biology suggests an explanation for such a case. The classification of cerebrofacial venous metameric syndromes (CVMS) enables us to recognise this lesion as involving the most caudal of the cranial metamere (CVMS 3).
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Ramli, N., Sachet, M., Bao, C. et al. Cerebrofacial venous metameric syndrome (CVMS) 3: Sturge-Weber syndrome with bilateral lymphatic/venous malformations of the mandible. Neuroradiology 45, 687–690 (2003). https://doi.org/10.1007/s00234-003-1042-9
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DOI: https://doi.org/10.1007/s00234-003-1042-9