Case reportFibrous dysplasia with cystic appearance in maxillary sinus
Introduction
Fibrous dysplasia (FD) of the bone is a slowly progressive, benign disease of unknown cause where normal architectures are replaced with fibrous and osteoid tissue. The disease usually develops over several years in the first or second decades of life. Swelling without pain is the most common initial symptom, and malignant changes are rare.
There are three types of FD: monostotic, polyostotic, and McCune–Albright syndrome. Monostotic FD is predominant, and craniofacial involvement occurs in approximately 30% of the cases [1]. FD in the paranasal sinuses is uncommon, and its management may be difficult.
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Case history
In July 1995, a 25-year-old female complaining of a mild facial swelling on the left side was seen in Kawaguchi-Kogyo General Hospital. The swelling had been present for few years, and the patient also had a heavy feeling. The patient had no previous history of rhinosinusitis, craniofacial trauma or nasal surgery. Computed tomographic (CT) scans (Fig. 1, Fig. 2) and magnetic resonance (MR) images (Fig. 3, Fig. 4) showed a cystic lesion and dense bone changes in the maxillary bone.
An inferior
Discussion
Although, in the present case, the FD affected the maxillary bone itself and not the maxillary sinus, CT scans and MR images showed that the cystic lesion almost entirely occupied the maxillary sinus. Therefore, we considered this case as one FD in the maxillary sinus.
FD of the maxillary bone, which is the most commonly affected craniofacial bone, usually manifests as a painless facial deformity. However, the disease may also show symptoms like loosening of teeth and deformity of the alveolar
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