Pontine hypoplasia in a child with sensorineural deafness
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Cited by (20)
Contralateral non-auditory stimulation in auditory brainstem implantation: A case report
2019, International Journal of Pediatric OtorhinolaryngologyCitation Excerpt :Pontocerebellar hypoplasia is an inherited progressive neurodegenerative disorder with fetal onset associated with the hypoplasia/atrophy of cerebellum and pons, and other symptoms such as developmental delay [9]. Although the hearing loss was not commonly seen in pontocerebellar hypoplasia, the first case report with a combination of pontocerebellar hypoplasia and sensorineural hearing loss was presented in 1997 [10]. So far, 119 children with inner ear malformations have received ABIs at Hacettepe University.
Pontine tegmental cap dysplasia with a duplicated internal auditory canal
2019, Radiology Case ReportsCitation Excerpt :He will need special education and speech therapy as he gets older. The term PTCD was coined by Barth, et al. in 2007 in his report of 4 cases [10], though 2 potential cases of PTCD with similar hindbrain malformations and clinical findings were reported prior to 2007 [15–16]. On MRI, the hindbrain malformation is described as a flattened, hypoplastic ventral pons with a tegmental cap, a curved protrusion of the dorsal pons from the middle third of the tegmentum into the fourth ventricle [17].
Novel clinical features in pontine tegmental cap dysplasia
2012, Pediatric NeurologyCitation Excerpt :Few cases of pontine tegmental cap dysplasia have been described in the literature [1-11].
Inferior pontine segmentation abnormality in a child with sensorineural deafness: DTI analysis of fiber tracts
2011, Journal of NeuroradiologyCochlear implantation in pontine tegmental cap dysplasia
2010, International Journal of Pediatric OtorhinolaryngologyCitation Excerpt :Radiographic findings similar to those seen in PTCD have been noted in the literature twice before. In 1997, Maeoka et al. [2] reported the case of a 2-year-old girl with bilateral sensorineural deafness showing pontine hypoplasia and a bulging contour of the pontine tegmentum on MRI. In 2005, Ouanounou et al. [3] reported a case of Möbius syndrome in a 3-month-old male infant with pontine hypoplasia and complete absence of the middle cerebellar peduncles.
Pontine Tegmental Cap Dysplasia-the Role of MRI and DTI in Diagnosis
2020, Neurology India