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Audiological, vestibular and radiological abnormalities in Kallman's syndrome

Published online by Cambridge University Press:  29 June 2007

J. Hill ,
C. Elliott  and
I. Colquhoun
J. Hill*
Affiliation:
Department of Otolaryngology, Freeman Hospital.
C. Elliott
Affiliation:
Department of Medical Physics, Freeman Hospital.
I. Colquhoun
Affiliation:
Department of Radiology, Charing Cross Hospital, London.
*
J. Hill, F.R.C.S., Department of Otolaryngology, Freeman Hospital, High Heaton, Newcastle upon Tyne NE7 7DN.
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Abstract

Kallman's syndrome is a multifaceted congenital disorder with predominantly endocrine abnormalities. We have characterized the associated mixed hearing loss and identified consistent radiological evidence of abnormal temporal bone anatomy. Abnormal labyrinthine morphology is accompanied by a complete absence of response to vestibular stimulation with caloric or rotational chair testing.

The endocrine abnormalities are correctable and Kallman's syndrome is a diagnosis worthy of consideration when assessing children with congenital hearing loss.

Keywords

Kallman's SyndromeAudiologyRadiology
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 106 , Issue 6 , June 1992 , pp. 530 - 534
Copyright
Copyright © JLO (1984) Limited 1992

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