Klinefelter's syndrome, cerebral germinoma, Chiari malformation, and syrinx: a case report

Neurosurgery. 1986 Feb;18(2):220-2. doi: 10.1227/00006123-198602000-00021.

Abstract

A case of Klinefelter's syndrome associated with intracranial germinoma and Chiari malformation is described. The case is discussed in view of the literature linking Klinefelter's syndrome with skeletal defects and germinoma.

Publication types

  • Case Reports

MeSH terms

  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Arnold-Chiari Malformation / complications*
  • Bleomycin
  • Brain Neoplasms / complications*
  • Brain Neoplasms / pathology
  • Brain Neoplasms / therapy
  • Child
  • Cisplatin
  • Combined Modality Therapy
  • Dysgerminoma / complications*
  • Dysgerminoma / pathology
  • Dysgerminoma / therapy
  • Etoposide
  • Humans
  • Klinefelter Syndrome / complications*
  • Male
  • Spina Bifida Occulta / complications*

Substances

  • Bleomycin
  • Etoposide
  • Cisplatin

Supplementary concepts

  • BEP protocol