Abstract
Dermatofibrosarcoma protuberans is a tumor of intermediate malignancy characterized by its aggressive local growth and marked propensity to recur after surgical excision. This article reviews the incidence, clinical presentation, histologic features, immunocytochemical studies, histogenesis, prognosis, management, and follow-up recommendations for this unusual neoplasm.
Publication types
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Research Support, Non-U.S. Gov't
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Review
MeSH terms
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Cell Lineage
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Dermatofibrosarcoma / diagnosis
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Dermatofibrosarcoma / pathology*
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Dermatofibrosarcoma / surgery
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Follow-Up Studies
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Humans
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Immunohistochemistry
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Incidence
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Neoplasm Invasiveness
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Neoplasm Recurrence, Local / pathology
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Prognosis
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Skin Neoplasms / diagnosis
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Skin Neoplasms / pathology
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Skin Neoplasms / surgery