Dermatofibrosarcoma protuberans

J Am Acad Dermatol. 1996 Sep;35(3 Pt 1):355-74; quiz 375-6. doi: 10.1016/s0190-9622(96)90597-6.

Abstract

Dermatofibrosarcoma protuberans is a tumor of intermediate malignancy characterized by its aggressive local growth and marked propensity to recur after surgical excision. This article reviews the incidence, clinical presentation, histologic features, immunocytochemical studies, histogenesis, prognosis, management, and follow-up recommendations for this unusual neoplasm.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Cell Lineage
  • Dermatofibrosarcoma / diagnosis
  • Dermatofibrosarcoma / pathology*
  • Dermatofibrosarcoma / surgery
  • Follow-Up Studies
  • Humans
  • Immunohistochemistry
  • Incidence
  • Neoplasm Invasiveness
  • Neoplasm Recurrence, Local / pathology
  • Prognosis
  • Skin Neoplasms / diagnosis
  • Skin Neoplasms / pathology
  • Skin Neoplasms / surgery